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<article article-type="research-article" dtd-version="1.3" xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance" xml:lang="ru"><front><journal-meta><journal-id journal-id-type="publisher-id">thealth</journal-id><journal-title-group><journal-title xml:lang="ru">Здравоохранение Таджикистана</journal-title><trans-title-group xml:lang="en"><trans-title>Health care of Tajikistan</trans-title></trans-title-group></journal-title-group><issn pub-type="ppub">0514-2415</issn><publisher><publisher-name>Редакция журнала «Здравоохранение Таджикистана»</publisher-name></publisher></journal-meta><article-meta><article-id pub-id-type="doi">10.52888/0514-2515-2023-358-3-57-61</article-id><article-id custom-type="elpub" pub-id-type="custom">thealth-477</article-id><article-categories><subj-group subj-group-type="heading"><subject>Research Article</subject></subj-group><subj-group subj-group-type="section-heading" xml:lang="ru"><subject>Статьи</subject></subj-group></article-categories><title-group><article-title>Лечение болезни Гиршпрунга у детей раннего возраста</article-title><trans-title-group xml:lang="en"><trans-title>Treatment of Hirschsprung’s disease in young children</trans-title></trans-title-group></title-group><contrib-group><contrib contrib-type="author" corresp="yes"><name-alternatives><name name-style="eastern" xml:lang="ru"><surname>Мирзоев</surname><given-names>Д. С</given-names></name><name name-style="western" xml:lang="en"><surname>Mirzoev</surname><given-names>D. S.</given-names></name></name-alternatives><bio xml:lang="ru"><p>Мирзоев Довуд Саидназарович –кандидат медицинских наук, докторант кафедры общая хирургии НОУ «Медико-социалный институт Таджикистана»</p></bio><bio xml:lang="en"><p>Mirzoev Dovud Saidnazarovich  - Candidate of Medical Sciences, doctoral student of the Department of General Surgery of NEI “Medical and Social Institute of Tajikistan”; </p></bio><email xlink:type="simple">dovudshoh73@mail.ru</email><xref ref-type="aff" rid="aff-1"/></contrib><contrib contrib-type="author" corresp="yes"><name-alternatives><name name-style="eastern" xml:lang="ru"><surname>Ибодов</surname><given-names>Х.</given-names></name><name name-style="western" xml:lang="en"><surname>Ibodov</surname><given-names>H.</given-names></name></name-alternatives><xref ref-type="aff" rid="aff-2"/></contrib><contrib contrib-type="author" corresp="yes"><name-alternatives><name name-style="eastern" xml:lang="ru"><surname>Яхшибекова</surname><given-names>Ш. Дж.</given-names></name><name name-style="western" xml:lang="en"><surname>Yakhshibekova</surname><given-names>Sh. I.</given-names></name></name-alternatives><xref ref-type="aff" rid="aff-1"/></contrib><contrib contrib-type="author" corresp="yes"><name-alternatives><name name-style="eastern" xml:lang="ru"><surname>Рофиев</surname><given-names>Р. Р.</given-names></name><name name-style="western" xml:lang="en"><surname>Rofiev</surname><given-names>R. R.</given-names></name></name-alternatives><xref ref-type="aff" rid="aff-3"/></contrib><contrib contrib-type="author" corresp="yes"><name-alternatives><name name-style="eastern" xml:lang="ru"><surname>Икромов</surname><given-names>Т. Ш.</given-names></name><name name-style="western" xml:lang="en"><surname>Kromov</surname><given-names>T. Sh.</given-names></name></name-alternatives><xref ref-type="aff" rid="aff-4"/></contrib><contrib contrib-type="author" corresp="yes"><name-alternatives><name name-style="eastern" xml:lang="ru"><surname>Латипов</surname><given-names>Ш Э.</given-names></name><name name-style="western" xml:lang="en"><surname>Latipov</surname><given-names>Sh. E.</given-names></name></name-alternatives><xref ref-type="aff" rid="aff-3"/></contrib></contrib-group><aff-alternatives id="aff-1"><aff xml:lang="ru"><institution>НОУ «Медико – социальный институт Таджикистана»; &#13;
ГУ «Республиканский научно-клинический центр педиатрии и детской хирургии»</institution><country>Таджикистан</country></aff><aff xml:lang="en"><institution>NEI “Medical and Social Institute of Tajikistan”; &#13;
SI “Republican Scientific-Clinical Center of Pediatrics and Children’s Surgery”</institution><country>Tajikistan</country></aff></aff-alternatives><aff-alternatives id="aff-2"><aff xml:lang="ru"><institution>НОУ «Медико – социальный институт Таджикистана»; &#13;
ГОУ «Институт последипломного подготовки медицинских кадров в сфере здравоохранения Республики Таджикистана»</institution><country>Таджикистан</country></aff><aff xml:lang="en"><institution>NEI “Medical and Social Institute of Tajikistan”; &#13;
SEI “Institute of postgraduate training of medical personnel in the field of health care of the Republic of Tajikistan”</institution><country>Tajikistan</country></aff></aff-alternatives><aff-alternatives id="aff-3"><aff xml:lang="ru"><institution>НОУ «Медико – социальный институт Таджикистана»</institution><country>Таджикистан</country></aff><aff xml:lang="en"><institution>NEI “Medical and Social Institute of Tajikistan”</institution><country>Tajikistan</country></aff></aff-alternatives><aff-alternatives id="aff-4"><aff xml:lang="ru"><institution>ГОУ «Институт последипломного подготовки медицинских кадров в сфере здравоохранения Республики Таджикистана»; &#13;
ГУ «Республиканский научно-клинический центр педиатрии и детской хирургии»</institution><country>Таджикистан</country></aff><aff xml:lang="en"><institution>SEI “Institute of postgraduate training of medical personnel in the field of health care of the Republic of Tajikistan”; &#13;
SI “Republican Scientific-Clinical Center of Pediatrics and Children’s Surgery”</institution><country>Tajikistan</country></aff></aff-alternatives><pub-date pub-type="collection"><year>2023</year></pub-date><pub-date pub-type="epub"><day>09</day><month>11</month><year>2023</year></pub-date><volume>0</volume><issue>3</issue><fpage>57</fpage><lpage>61</lpage><permissions><copyright-statement>Copyright &amp;#x00A9; Мирзоев Д.С., Ибодов Х., Яхшибекова Ш.Д., Рофиев Р.Р., Икромов Т.Ш., Латипов Ш.Э., 2023</copyright-statement><copyright-year>2023</copyright-year><copyright-holder xml:lang="ru">Мирзоев Д.С., Ибодов Х., Яхшибекова Ш.Д., Рофиев Р.Р., Икромов Т.Ш., Латипов Ш.Э.</copyright-holder><copyright-holder xml:lang="en">Mirzoev D.S., Ibodov H., Yakhshibekova S.I., Rofiev R.R., kromov T.S., Latipov S.E.</copyright-holder><license xml:lang="ru" license-type="creative-commons-attribution" xlink:href="https://creativecommons.org/licenses/by/4.0/" xlink:type="simple"><license-p>Данная работа распространяется под лицензией Creative Commons Attribution 4.0.</license-p></license><license xml:lang="en" license-type="creative-commons-attribution" xlink:href="https://creativecommons.org/licenses/by/4.0/" xlink:type="simple"><license-p>This work is licensed under a Creative Commons Attribution 4.0 License.</license-p></license></permissions><self-uri xlink:href="https://www.zdrav.tj/jour/article/view/477">https://www.zdrav.tj/jour/article/view/477</self-uri><abstract><sec><title>Цель исследования</title><p>Цель исследования. Оптимизации лечения болезни Гиршпрунга у детей раннего возраста.</p><p>Материал и методы исследование. Под наблюдение находилось 71 детей в возрасте от 3 дней до 3 лет. Больные были разделены на 3 группы, по виду выполнение операции: методом трансанальной эндоректальной проктопластики по De La Torre–Mondragon у 23 (32,4%) детей, по Swenson like у 17 (23,9%) и по Соаве-Ленюшкина</p></sec><sec><title>у 31 (43,7%) детей</title><p>у 31 (43,7%) детей.</p><p>Результаты исследование и их обсуждение. В результатах исследования у матери выявили наличие цитомегаловируса, вируса герпеса и токсоплазмоза. Основой успешности хирургического лечение является своевременное установление диагноза. После проведение оперативного вмешательства гистологическое исследование операционного материала подтвердило аганглиоз кишечника. Брюшинно-промежностная проктопластика по Соаве-Ленюшкина в модификации клиники, с клиновидным иссечением серозно-мышечного футляра, эффективна в плане профилактика межфутлярных гематом и скоплении жидкости. Методика трансанально эндоректального низведение De La TorreMondragon и Swenson-like, без брюшного доступа с демукозацийе прямой кишки, считается эффективным и малоинвазивным доступом при ректальной и ректосигмоидальной форме болезни Гиршпрунга.</p></sec><sec><title>Выводы</title><p>Выводы. Проведение трансанально эндоректального низведение в раннем возрасте у детей показал скорое востановление моторики кишечника в послеоперационном периоде без разреза кожных покров. Результаты раннего проведение оперативного вмешательства способствуют достижению хороших результатов в ближайшем и отдалённом периоде после оперативного вмешательства.</p></sec></abstract><trans-abstract xml:lang="en"><sec><title>Objective</title><p>Objective. The objective of this study was to optimize the treatment for Hirschsprung’s disease in young children.</p></sec><sec><title>Material and methods</title><p>Material and methods. A total of 71 children, ranging in age from 3 days to 3 years, were observed. Patients were categorized into three groups based on the surgical procedure performed: 23 underwent transanal endorectal proctoplasty according to De La Torre Mondragon (32.4%), 17 according to the Swenson-like method (23.9%), and 31 according to Soave-Lenyushkin (43.7%).</p></sec><sec><title>Results and discussion</title><p>Results and discussion. The results of the maternal examination revealed the presence of cytomegalovirus, herpes virus and toxoplasmosis. The basis for the success of surgical treatment is timely diagnosis. After surgical intervention, histological examination of the surgical material confirmed intestinal agangliosis. Peritoneal-promesenteric proctoplasty according to SoaveLenyushkin in the modification of the clinic, with wedge-shaped excision of the serous-muscular case, is effective in terms of prevention of inter-sheath hematomas and fluid accumulation. The De La Torre-Mondragon and Swenson-like technique of transanal endorectal relegation, without abdominal access with demucosation of the rectum, is considered an effective and minimally invasive access for rectal and rectosigmoidal forms of Hirschsprung’s disease.</p></sec><sec><title>Conclusions</title><p>Conclusions. Transanal endorectal relegation at an early age in children showed rapid recovery of intestinal motility in the postoperative period without skin incision. The results of early surgical intervention contribute to the achievement of good results in the immediate and distant period after the surgical intervention.</p></sec></trans-abstract><kwd-group xml:lang="ru"><kwd>болезнь Гиршпрунга</kwd><kwd>трансанально эндоректальное</kwd><kwd>брюшино-промежностное</kwd><kwd>демукозация</kwd><kwd>аганглиоз</kwd><kwd>дети</kwd></kwd-group><kwd-group xml:lang="en"><kwd>Hirschsprung disease</kwd><kwd>transanal endorectal</kwd><kwd>peritoneal-perineal</kwd><kwd>demucosation</kwd><kwd>agangliosis</kwd><kwd>children.</kwd></kwd-group></article-meta></front><back><ref-list><title>References</title><ref id="cit1"><label>1</label><citation-alternatives><mixed-citation xml:lang="ru">Ахпаров Н Н, Улучшение результатов хирургического лечения болезни Гиршпрунга у детей. / Н.Н. Ахпаров, М.М. Калабаева, К.Э. Хаиров // Педиатрия и детская хирургия. 2019, №2, – С. 42</mixed-citation><mixed-citation xml:lang="en">Akhparov N.N. 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