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Hirschsprung’s disease in newborns: diseases-”Masks”

https://doi.org/10.52888/0514-2515-2024-361-2-94-100

Abstract

 Two clinical cases of manifestation of clinical symptoms of Hirschsprung’s disease in infants in the form of necrotising enterocolitis in a premature newborn with spontaneous perforation of the terminal ileum and subsequent multiple surgical interventions due to recurrent perforations, failure of  anastomoses after intestinal tube reconstructions are described. The casuistic occurrence of the perforative form of acute appendicitis in a newborn of 3 days of age, the subsequent increasing clinical picture of intestinal dysfunction, considered as “peritoneal adhesions” - a rare example of the onset and course of colonic agangliosis. 

About the Authors

N. M. Stepanova
Irkutsk Municipal Pediatric Clinical Hospital; Irkutsk State Medical University
Russian Federation

Stepanova Natalia Maratovna - Candidate of Medical Sciences, Associate Professor, Department of Paediatric Surgery

Tel.: +79245301973 

Irkutsk



V. A. Novozilov
Irkutsk Municipal Pediatric Clinical Hospital; Irkutsk State Medical University; Irkutsk State Medical Academy of Postgraduate Education
Russian Federation

Irkutsk



Yu. I. Petrova
Irkutsk State Medical University
Russian Federation

Irkutsk



Yu. A. Telnova
Irkutsk State Medical University
Russian Federation

Irkutsk



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Review

For citations:


Stepanova N.M., Novozilov V.A., Petrova Yu.I., Telnova Yu.A. Hirschsprung’s disease in newborns: diseases-”Masks”. Health care of Tajikistan. 2024;(2):94-100. (In Russ.) https://doi.org/10.52888/0514-2515-2024-361-2-94-100

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ISSN 0514-2415 (Print)