Early diagnosis and surgical treatment of Hirschsprung’s disease in newborns
https://doi.org/10.52888/0514-2515-2021-349-2-23-29
Abstract
Aim. Improve the results of diagnosis and surgical treatment of Hirschsprung’s disease in the neonatal period.
Materials and methods. The article presents an analysis of the diagnosis and results of surgical treatment of 15 children with Hirschsprung’s disease in the neonatal period, in the Department of Neonatology and Neonatal Surgery of the Scientific Center of Pediatrics and Pediatric Surgery from 2017 to 2020.
Results. All children were found to have a rectosigmoid form of the disease. 10 (66.6%) newborns underwent radical surgery-transanal endorectal proctoplasty according to Svenson-like. Immunohistochemical examination with the use of calretinin confirmed Hirschsprung’s disease in all operated children.
Conclusions. Our results of surgical treatment in the neonatal period indicate that early diagnosis and early surgical correction contribute to the rapid restoration of gastrointestinal motility, and the method of choice is Svensonlike transanal endorectal proctoplasty, which has proven to be an effective and gentle method of surgical correction for this pathology. Also, the use of immunohistochemical studies with calretinin is a highly sensitive diagnostic method.
About the Authors
N. N. Akhparov
JSC «Scientific Center of Pediatrics and Pediatric Surgery»
Tajikistan
Tajikistan
Akhparov Nurlan Nurkеnovich - Doctor of Medical Sciences, Professor, Head of the Department of Surgery of the Scientific Center of Pediatrics and Pediatric Surgery
Almaty, Al-farabi 146, phone: 87272990679
G. T. Kaukenbayeva
JSC «Scientific Center of Pediatrics and Pediatric Surgery»
Tajikistan
Tajikistan
Almaty, Al-farabi 146
M. M. Kalabaeva
JSC «Scientific Center of Pediatrics and Pediatric Surgery»
Tajikistan
Tajikistan
Almaty, Al-farabi 146
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Review
For citations:
Akhparov N.N., Kaukenbayeva G.T., Kalabaeva M.M. Early diagnosis and surgical treatment of Hirschsprung’s disease in newborns. Health care of Tajikistan. 2021;(2):23-29. (In Russ.) https://doi.org/10.52888/0514-2515-2021-349-2-23-29
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